Ependymoblastoma (WHO grade IV) or supratentorial primitive neuroectodermal tumor is a rare, malignant, embryonal brain tumor that occurs in neonates and young children (Becker et al. 2000).

Ependymoblastomas are often large and supratentorial and generally relate to the ventricles, although they do occur at other sites.

These types of tumors grow rapidly, with craniospinal dissemination, and have a fatal outcome within 6 to 12 months of diagnosis. There are only a limited number of imaging studies available in this tumor. A recent study by Chawla et al. (2007) found that ependymoblastomas present as large, vascular, and hemorrhagic tumors. Due to the high cellular density, the tumors appear isointense to gray matter with a strong enhancement pattern.